Friedreich's Ataxia Life Expectancy at Life

Friedreich's Ataxia Life Expectancy. Friedreich ataxia can shorten life expectancy, and heart disease is the most common cause of death. Friedreich ataxia (frda) is an inherited neurodegenerative disorder classically characterized by progressive gait and limb ataxia, dysarthria, dysphagia, oculomotor dysfunction, loss of deep tendon reflexes, pyramidal tract signs, scoliosis, and in some, cardiomyopathy, diabetes mellitus, visual loss and defective hearing.

Nearly 60% of deaths are cardiac in nature, with 1 in 8 deaths due to arrhythmia. Friedreich ataxia can shorten life expectancy, and heart disease is the most common cause of death. Generally, within 10 to 20 years after the appearance of the first symptoms the person is confined to a wheelchair.

PPT Scoliosis in children and adolescents with

Later in the disease, those affected may become incapacitated. Aims friedreich ataxia (frda) is the most commonly inherited ataxia; As discussed previously, the rate at which the symptoms worsen varies among affected people. Friedreich's ataxia (fa) is an inherited disease that damages the nervous system.